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KMID : 0359720230410010031
Journal of the Korean Neurological Association
2023 Volume.41 No. 1 p.31 ~ p.34
A Case of Inclusion Body Myositis with Clinical, Pathological and Serological Consideration
Park Yeong-Eun

Kang Min-Sung
Shin Jin-Hong
Kim Dae-Sung
Abstract
Inclusion body myositis is a rare condition of idiopathic inflammatory myopathy. Prior criteria for the diagnosis of inclusion body myositis essentially required pathological features of rimmed vacuoles, tubulofilamentous inclusions, and amyloid deposits. However, recently developed new diagnostic criteria emphasize clinical characteristics including weakness of finger flexors and knee extensors. In addition, a serological evaluation of anti-cN1A antibody is helpful for the diagnosis. We report a case of inclusion body myositis with clinical, pathological, and serological consideration.
KEYWORD
Inclusion body myositides, Pathology, Antibodies
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