KMID : 0359720230410010031
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Journal of the Korean Neurological Association 2023 Volume.41 No. 1 p.31 ~ p.34
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A Case of Inclusion Body Myositis with Clinical, Pathological and Serological Consideration
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Park Yeong-Eun
Kang Min-Sung Shin Jin-Hong Kim Dae-Sung
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Abstract
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Inclusion body myositis is a rare condition of idiopathic inflammatory myopathy. Prior criteria for the diagnosis of inclusion body myositis essentially required pathological features of rimmed vacuoles, tubulofilamentous inclusions, and amyloid deposits. However, recently developed new diagnostic criteria emphasize clinical characteristics including weakness of finger flexors and knee extensors. In addition, a serological evaluation of anti-cN1A antibody is helpful for the diagnosis. We report a case of inclusion body myositis with clinical, pathological, and serological consideration.
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KEYWORD
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Inclusion body myositides, Pathology, Antibodies
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